This is a hereditary condition that usually manifests itself in early childhood. It consists of cutaneous and subcutaneous tumors composed of nodules of fibroblasts in a hyalinized, collagenized stroma. It is a rare condition, and patients usually present with multiple painless skin or subcutaneous nodules. These nodules vary from a few millimeters to 5 cm in diameter. The most commonly affected sites include the head and neck, back, and lower extremities. Most of these lesions are removed for cosmetic reasons; if they cause no detriment to function, they may be left alone.